Improved Survival in Fontan-Associated Protein-Losing Enteropathy∗
نویسندگان
چکیده
منابع مشابه
Clinical outcomes and improved survival in patients with protein-losing enteropathy after the Fontan operation.
BACKGROUND Patients with protein-losing enteropathy (PLE) following the Fontan operation have a reported 50% mortality at 5 years after diagnosis. OBJECTIVES The aim of this study was to review outcomes in patients with PLE following the Fontan operation. METHODS From 1992 to 2010, 42 patients (55% male) with PLE following the Fontan operation were identified from clinical databases at the ...
متن کاملProtein-losing enteropathy after the Fontan operation.
Patients were observed after the Fontan operation to determine the frequency and severity of protein-losing enteropathy. A total of 427 patients who survived for 30 days after the Fontan operation, performed between 1973 and January 1987, were analyzed and, thus far, protein-losing enteropathy has developed in 47 of 427. The cumulative risk for the development of protein-losing enteropathy by 1...
متن کاملProtein Losing Enteropathy after Fontan Surgery – Clinical and Diagnostical Aspects
Protein losing enteropathy (PLE) is the massive enteric loss of serum protein. PLE may appear in several diseases associated with intestinal mucous membrane damages with or without infection. PLE is mostly associated with total cavopulmonary connection (TCPC) or Fontan-type circulation in patients with a functionally univentricular heart. TCPC is performed at an age of about 2 years or older an...
متن کاملGastrointestinal haemorrhage in protein-losing enteropathy associated with the Fontan circulation.
A 29-year-old patient was born with a double inlet left ventricle with transposition of the great arteries and pulmonary valvular stenosis. This was initially treated with a right modified Blalock–Taussig shunt, and 2 years later he underwent a Fontan operation. Aged 13 years he had an aortic valve replacement with reconstruction of his Fontan circulation, making it more haemodynamically stream...
متن کاملProtein losing enteropathy associated with collagen diseases.
Four patients with collagen diseases are described, who developed protein losing enteropathy in the course of their disease. Their protein losing enteropathies subsided after treatment with 60 mg/day oral prednisolone. Immunohistological studies of the small intestine showed deposits of C3 in the capillary walls of villi in two patients. Increased capillary permeability due to autoimmune phenom...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Journal of the American College of Cardiology
سال: 2014
ISSN: 0735-1097
DOI: 10.1016/j.jacc.2014.05.002